Cystic fibrosis in 3 Pakistani children.

Cystic fibrosis in 3 Pakistani children.

Prevalence of Cystic Fibrosis Trans-membrane Conductance Regulator Gene common mutations in children with cystic fibrosis in Isfahan, Iran

Background: Cystic fibrosis (CF) is the most common lethal genetic disorder of Cystic Fibrosis Trans-membrane Conductance (CFTR) Regulator gene mutations. We aimed to investigate common mutations in CF patients and to assess its possible relationship with clinical presentations. Materials and Methods: This cross sectional study was conducted on 36 CF patients who were referred to a tertiary ped...

CYSTIC FIBROSIS Airway remodelling in children with cystic fibrosis

Background: The relationship between airway structural changes and inflammation is unclear in early cystic fibrosis (CF) lung disease. A study was undertaken to determine changes in airway remodelling in children with CF compared with appropriate disease and healthy controls. Methods: Bronchoalveolar lavage and endobronchial biopsy were performed in a cross-sectional study of 43 children with C...

Maintaining Respiratory Health in Cystic Fibrosis Patients

Cystic fibrosis (CF) is an inherited disease that primarily affects the lungs and the digestive system, however, it also affects a number of other organs and systems. More than 90% of mortality of  CF patients is due to lung complications.  Healthy lungs are important for a long life for people with CF, We will discuss two important topics for maintaining respiratory health. Chronic use of drug...

evaluating the effects of omega-3 on quality of life in children with cystic fibrosis

background : cystic fibrosis (cf) is an autosomal recessive disorder chiefly characterized by respiratory and gastrointestinal symptoms. this study investigates whether omega-3 fatty acid affects quality of life in children with cf. materials and methods: this was a single-blind, pilot study undertaken at the cystic fibrosis center of sarvar children hospital, mashhad, iran from march 2009 unti...